Case of the Month

Rizzoli Case 10

A 39 year old woman had a history of shortened, deformed extremities and had previously had corrective surgery. The hand radiograph showed multiple characteristic radiographic features and it should immediately confirm the diagnosis. Seen in the radiograph of the distal femur is an additional "classic" radiographic feature of this condition that has been described as "sled runner tracks". An AP radiograph of the pelvis is also shown.

The patient now presents complaining of left hip pain at the side of a lesion that has previously been operated. A radiograph of the hip and two CT images are shown.

An additional CT image shows the scar from the previous surgical procedure and its relationship to the left hip lesion.

1) What is the diagnosis?

2) Is this condition hereditary?

3) What is the lesion in the left hip?

Send in you answers to questions@bonetumor.org or click on the link below. Include "Rizzoli Case 10" in the text.

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